Periodic and Non-Periodic Fevers

This book, written by very well-known opinion leaders in the field, covers all aspects of periodic and non -periodic fevers, and related disorders. The expression refers to several different auto-inflammatory diseases, showing similar symptoms-the primary symptom being a recurrent fever for an infec...

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Detalles Bibliográficos
Autor Corporativo: SpringerLink (-)
Otros Autores: Cimaz, Rolando (-)
Formato: Libro electrónico
Idioma:Inglés
Publicado: Cham : Springer International Publishing 2020.
Edición:1st ed
Colección:Springer eBooks.
Rare Diseases of the Immune System ;
Acceso en línea:Conectar con la versión electrónica
Ver en Universidad de Navarra:https://innopac.unav.es/record=b43244580*spi
Tabla de Contenidos:
  • Preface
  • I From Pathogenesis to Classification
  • 1 Historical notes on Autoinflammatory disorders
  • 2 Pathogenesis:Genetic basis, Innate Immunity, Inflammosomes, Cytokines
  • 3 Classification and nomenclature of Periodic and Non Periodic fevers
  • II Specific diseases
  • 4 Mevalonate Kinase Deficiency (MKD)
  • 5 Tumor necrosis factor receptors associated syndrome (TRAPS)
  • 6 Cryopyrin-Associated Periodic Syndromes (CAPS)
  • 7 Pyogenic Arthritis, Pyoderma gangrenosum and Acne Syndrome (PAPA)
  • 8 Adenosine deaminase syndrome 2 (ADA2)
  • 9 Interferonopathies
  • 10 Inflammatory bone disease
  • 11 Amyloidosis
  • 12 Dermatologic autoinflammatory diseases
  • 13 Autoinflammatory diseases with immunodeficiency
  • 14 Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis Syndrome (PFAPA)
  • 15 Proteasome. related disorders
  • 16 Chronic Non-bacterial osteomyelitis
  • 17 Systemic JIA and adult onset Still disease
  • 18 Behcet disease
  • 19 Recurrent idiopathic pericarditis
  • 20 Schnitzler syndrome
  • Subject Index.