Periodic and Non-Periodic Fevers
This book, written by very well-known opinion leaders in the field, covers all aspects of periodic and non -periodic fevers, and related disorders. The expression refers to several different auto-inflammatory diseases, showing similar symptoms-the primary symptom being a recurrent fever for an infec...
Autor Corporativo: | |
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Otros Autores: | |
Formato: | Libro electrónico |
Idioma: | Inglés |
Publicado: |
Cham :
Springer International Publishing
2020.
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Edición: | 1st ed |
Colección: | Springer eBooks.
Rare Diseases of the Immune System ; |
Acceso en línea: | Conectar con la versión electrónica |
Ver en Universidad de Navarra: | https://innopac.unav.es/record=b43244580*spi |
Tabla de Contenidos:
- Preface
- I From Pathogenesis to Classification
- 1 Historical notes on Autoinflammatory disorders
- 2 Pathogenesis:Genetic basis, Innate Immunity, Inflammosomes, Cytokines
- 3 Classification and nomenclature of Periodic and Non Periodic fevers
- II Specific diseases
- 4 Mevalonate Kinase Deficiency (MKD)
- 5 Tumor necrosis factor receptors associated syndrome (TRAPS)
- 6 Cryopyrin-Associated Periodic Syndromes (CAPS)
- 7 Pyogenic Arthritis, Pyoderma gangrenosum and Acne Syndrome (PAPA)
- 8 Adenosine deaminase syndrome 2 (ADA2)
- 9 Interferonopathies
- 10 Inflammatory bone disease
- 11 Amyloidosis
- 12 Dermatologic autoinflammatory diseases
- 13 Autoinflammatory diseases with immunodeficiency
- 14 Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis Syndrome (PFAPA)
- 15 Proteasome. related disorders
- 16 Chronic Non-bacterial osteomyelitis
- 17 Systemic JIA and adult onset Still disease
- 18 Behcet disease
- 19 Recurrent idiopathic pericarditis
- 20 Schnitzler syndrome
- Subject Index.